Splenectomy (surgical removal of the spleen) cures the anemia of spherocytosis. Although the abnormal cell defect persists, the red cell life span returns to normal.
Families with a history of spherocytosis should have their children screened for this disorder. In mild cases discovered in adult life, splenectomy may not be necessary.
Splenectomy should be delayed in children until the age of 5 to prevent unnecessary infection. Pneumococcal immunization (vaccine) is given prior to the surgery. Folic acid supplementation can be given to children.
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